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Times Cited: 526
Times Cited
Times Co-cited
Similarity
Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion.
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Prevention and reversal of severe mitochondrial cardiomyopathy by gene therapy in a mouse model of Friedreich's ataxia.
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Frataxin is reduced in Friedreich ataxia patients and is associated with mitochondrial membranes.
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GAA repeat expansion mutation mouse models of Friedreich ataxia exhibit oxidative stress leading to progressive neuronal and cardiac pathology.
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The role of oxidative stress in Friedreich's ataxia.
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Physiologically relevant reconstitution of iron-sulfur cluster biosynthesis uncovers persulfide-processing functions of ferredoxin-2 and frataxin.
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Mitochondrial iron trafficking and the integration of iron metabolism between the mitochondrion and cytosol.
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Frataxin activates mitochondrial energy conversion and oxidative phosphorylation.
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Rapid and Complete Reversal of Sensory Ataxia by Gene Therapy in a Novel Model of Friedreich Ataxia.
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Causative role of oxidative stress in a Drosophila model of Friedreich ataxia.
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Deferiprone in Friedreich ataxia: a 6-month randomized controlled trial.
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Co-cited is the co-citation frequency, indicating how many articles cite the article together with the query article. Similarity is the co-citation as percentage of the times cited of the query article or the article in the search results, whichever is the lowest. These numbers are calculated for the last 100 citations when articles are cited more than 100 times.