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Times Cited: 133
Times Cited: 133
Times Cited
Times Co-cited
Similarity
Oxidative stress in patients with Friedreich ataxia.
J B Schulz, T Dehmer, L Schöls, H Mende, C Hardt, M Vorgerd, K Bürk, W Matson, J Dichgans, M F Beal,[...]. Neurology 2000
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Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion.
V Campuzano, L Montermini, M D Moltò, L Pianese, M Cossée, F Cavalcanti, E Monros, F Rodius, F Duclos, A Monticelli,[...]. Science 1996
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Increased levels of plasma malondialdehyde in Friedreich ataxia.
M Emond, G Lepage, M Vanasse, M Pandolfo. Neurology 2000
M Emond, G Lepage, M Vanasse, M Pandolfo. Neurology 2000
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Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia.
A Rötig, P de Lonlay, D Chretien, F Foury, M Koenig, D Sidi, A Munnich, P Rustin. Nat Genet 1997
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Actin glutathionylation increases in fibroblasts of patients with Friedreich's ataxia: a potential role in the pathogenesis of the disease.
Anna Pastore, Giulia Tozzi, Laura Maria Gaeta, Enrico Bertini, Valentina Serafini, Silvia Di Cesare, Valentina Bonetto, Filippo Casoni, Rosalba Carrozzo, Giorgio Federici,[...]. J Biol Chem 2003
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The Friedreich's ataxia mutation confers cellular sensitivity to oxidant stress which is rescued by chelators of iron and calcium and inhibitors of apoptosis.
A Wong, J Yang, P Cavadini, C Gellera, B Lonnerdal, F Taroni, G Cortopassi. Hum Mol Genet 1999
A Wong, J Yang, P Cavadini, C Gellera, B Lonnerdal, F Taroni, G Cortopassi. Hum Mol Genet 1999
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Disabled early recruitment of antioxidant defenses in Friedreich's ataxia.
K Chantrel-Groussard, V Geromel, H Puccio, M Koenig, A Munnich, A Rötig, P Rustin. Hum Mol Genet 2001
K Chantrel-Groussard, V Geromel, H Puccio, M Koenig, A Munnich, A Rötig, P Rustin. Hum Mol Genet 2001
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Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits.
H Puccio, D Simon, M Cossée, P Criqui-Filipe, F Tiziano, J Melki, C Hindelang, R Matyas, P Rustin, M Koenig. Nat Genet 2001
H Puccio, D Simon, M Cossée, P Criqui-Filipe, F Tiziano, J Melki, C Hindelang, R Matyas, P Rustin, M Koenig. Nat Genet 2001
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Clinical, biochemical and molecular genetic correlations in Friedreich's ataxia.
J L Bradley, J C Blake, S Chamberlain, P K Thomas, J M Cooper, A H Schapira. Hum Mol Genet 2000
J L Bradley, J C Blake, S Chamberlain, P K Thomas, J M Cooper, A H Schapira. Hum Mol Genet 2000
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Frataxin is reduced in Friedreich ataxia patients and is associated with mitochondrial membranes.
V Campuzano, L Montermini, Y Lutz, L Cova, C Hindelang, S Jiralerspong, Y Trottier, S J Kish, B Faucheux, P Trouillas,[...]. Hum Mol Genet 1997
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Clinical and genetic abnormalities in patients with Friedreich's ataxia.
A Dürr, M Cossee, Y Agid, V Campuzano, C Mignard, C Penet, J L Mandel, A Brice, M Koenig. N Engl J Med 1996
A Dürr, M Cossee, Y Agid, V Campuzano, C Mignard, C Penet, J L Mandel, A Brice, M Koenig. N Engl J Med 1996
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Impaired nuclear Nrf2 translocation undermines the oxidative stress response in Friedreich ataxia.
Vincent Paupe, Emmanuel P Dassa, Sergio Goncalves, Françoise Auchère, Maria Lönn, Arne Holmgren, Pierre Rustin. PLoS One 2009
Vincent Paupe, Emmanuel P Dassa, Sergio Goncalves, Françoise Auchère, Maria Lönn, Arne Holmgren, Pierre Rustin. PLoS One 2009
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GAA repeat expansion mutation mouse models of Friedreich ataxia exhibit oxidative stress leading to progressive neuronal and cardiac pathology.
Sahar Al-Mahdawi, Ricardo Mouro Pinto, Dhaval Varshney, Lorraine Lawrence, Margaret B Lowrie, Sian Hughes, Zoe Webster, Julian Blake, J Mark Cooper, Rosalind King,[...]. Genomics 2006
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Regulation of mitochondrial iron accumulation by Yfh1p, a putative homolog of frataxin.
M Babcock, D de Silva, R Oaks, S Davis-Kaplan, S Jiralerspong, L Montermini, M Pandolfo, J Kaplan. Science 1997
M Babcock, D de Silva, R Oaks, S Davis-Kaplan, S Jiralerspong, L Montermini, M Pandolfo, J Kaplan. Science 1997
22
Antioxidant enzymes in blood of patients with Friedreich's ataxia.
G Tozzi, M Nuccetelli, M Lo Bello, S Bernardini, L Bellincampi, S Ballerini, L M Gaeta, C Casali, A Pastore, G Federici,[...]. Arch Dis Child 2002
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Glutathione-dependent redox status of frataxin-deficient cells in a yeast model of Friedreich's ataxia.
Françoise Auchère, Renata Santos, Sara Planamente, Emmanuel Lesuisse, Jean-Michel Camadro. Hum Mol Genet 2008
Françoise Auchère, Renata Santos, Sara Planamente, Emmanuel Lesuisse, Jean-Michel Camadro. Hum Mol Genet 2008
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Friedreich ataxia: the oxidative stress paradox.
Hervé Seznec, Delphine Simon, Cécile Bouton, Laurence Reutenauer, Ariane Hertzog, Pawel Golik, Vincent Procaccio, Manisha Patel, Jean-Claude Drapier, Michel Koenig,[...]. Hum Mol Genet 2005
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18
Frataxin-mediated iron delivery to ferrochelatase in the final step of heme biosynthesis.
Taejin Yoon, J A Cowan. J Biol Chem 2004
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Friedreich's ataxia: a clinical and genetic study of 90 families with an analysis of early diagnostic criteria and intrafamilial clustering of clinical features.
A E Harding. Brain 1981
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Causative role of oxidative stress in a Drosophila model of Friedreich ataxia.
José V Llorens, Juan A Navarro, Maria J Martínez-Sebastián, Mary K Baylies, S Schneuwly, José A Botella, Maria D Moltó. FASEB J 2007
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Friedreich ataxia: molecular mechanisms, redox considerations, and therapeutic opportunities.
Renata Santos, Sophie Lefevre, Dominika Sliwa, Alexandra Seguin, Jean-Michel Camadro, Emmanuel Lesuisse. Antioxid Redox Signal 2010
Renata Santos, Sophie Lefevre, Dominika Sliwa, Alexandra Seguin, Jean-Michel Camadro, Emmanuel Lesuisse. Antioxid Redox Signal 2010
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Frataxin deficiency leads to defects in expression of antioxidants and Nrf2 expression in dorsal root ganglia of the Friedreich's ataxia YG8R mouse model.
Yuxi Shan, Robert A Schoenfeld, Genki Hayashi, Eleonora Napoli, Tasuku Akiyama, Mirela Iodi Carstens, Earl E Carstens, Mark A Pook, Gino A Cortopassi. Antioxid Redox Signal 2013
Yuxi Shan, Robert A Schoenfeld, Genki Hayashi, Eleonora Napoli, Tasuku Akiyama, Mirela Iodi Carstens, Earl E Carstens, Mark A Pook, Gino A Cortopassi. Antioxid Redox Signal 2013
17
Oxidative stress, mitochondrial dysfunction and cellular stress response in Friedreich's ataxia.
Vittorio Calabrese, Raffaele Lodi, Caterina Tonon, Velia D'Agata, Maria Sapienza, Giovanni Scapagnini, Andrea Mangiameli, Giovanni Pennisi, A M Giuffrida Stella, D Allan Butterfield. J Neurol Sci 2005
Vittorio Calabrese, Raffaele Lodi, Caterina Tonon, Velia D'Agata, Maria Sapienza, Giovanni Scapagnini, Andrea Mangiameli, Giovanni Pennisi, A M Giuffrida Stella, D Allan Butterfield. J Neurol Sci 2005
15
Oxidative stress and protease dysfunction in the yeast model of Friedreich ataxia.
Anne-Laure Bulteau, Andrew Dancis, Monique Gareil, Jean-Jacques Montagne, Jean-Michel Camadro, Emmanuel Lesuisse. Free Radic Biol Med 2007
Anne-Laure Bulteau, Andrew Dancis, Monique Gareil, Jean-Jacques Montagne, Jean-Michel Camadro, Emmanuel Lesuisse. Free Radic Biol Med 2007
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Friedreich's ataxia: oxidative stress and cytoskeletal abnormalities.
Marco Sparaco, Laura Maria Gaeta, Filippo Maria Santorelli, Chiara Passarelli, Giulia Tozzi, Enrico Bertini, Alessandro Simonati, Francesco Scaravilli, Franco Taroni, Charles Duyckaerts,[...]. J Neurol Sci 2009
Marco Sparaco, Laura Maria Gaeta, Filippo Maria Santorelli, Chiara Passarelli, Giulia Tozzi, Enrico Bertini, Alessandro Simonati, Francesco Scaravilli, Franco Taroni, Charles Duyckaerts,[...]. J Neurol Sci 2009
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Deficit of in vivo mitochondrial ATP production in patients with Friedreich ataxia.
R Lodi, J M Cooper, J L Bradley, D Manners, P Styles, D J Taylor, A H Schapira. Proc Natl Acad Sci U S A 1999
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14
Increased glutathionyl hemoglobin in diabetes mellitus and hyperlipidemia demonstrated by liquid chromatography/electrospray ionization-mass spectrometry.
T Niwa, C Naito, A H Mawjood, K Imai. Clin Chem 2000
T Niwa, C Naito, A H Mawjood, K Imai. Clin Chem 2000
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Manganese superoxide dismutase induction by iron is impaired in Friedreich ataxia cells.
S Jiralerspong, B Ge, T J Hudson, M Pandolfo. FEBS Lett 2001
S Jiralerspong, B Ge, T J Hudson, M Pandolfo. FEBS Lett 2001
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Quantitation and characterization of glutathionyl haemoglobin as an oxidative stress marker in chronic renal failure by mass spectrometry.
Amit Kumar Mandal, Murali Woodi, Varun Sood, Patnam Rajagopalan Krishnaswamy, Anjali Rao, Sudarshan Ballal, Padmanabhan Balaram. Clin Biochem 2007
Amit Kumar Mandal, Murali Woodi, Varun Sood, Patnam Rajagopalan Krishnaswamy, Anjali Rao, Sudarshan Ballal, Padmanabhan Balaram. Clin Biochem 2007
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Redox environment of the cell as viewed through the redox state of the glutathione disulfide/glutathione couple.
F Q Schafer, G R Buettner. Free Radic Biol Med 2001
F Q Schafer, G R Buettner. Free Radic Biol Med 2001
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Hydrogen peroxide scavenging rescues frataxin deficiency in a Drosophila model of Friedreich's ataxia.
Peter R Anderson, Kim Kirby, William C Orr, Arthur J Hilliker, John P Phillips. Proc Natl Acad Sci U S A 2008
Peter R Anderson, Kim Kirby, William C Orr, Arthur J Hilliker, John P Phillips. Proc Natl Acad Sci U S A 2008
16
Altered gene expression and DNA damage in peripheral blood cells from Friedreich's ataxia patients: cellular model of pathology.
Astrid C Haugen, Nicholas A Di Prospero, Joel S Parker, Rick D Fannin, Jeff Chou, Joel N Meyer, Christopher Halweg, Jennifer B Collins, Alexandra Durr, Kenneth Fischbeck,[...]. PLoS Genet 2010
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16
RNAi-mediated suppression of the mitochondrial iron chaperone, frataxin, in Drosophila.
Peter R Anderson, Kim Kirby, Arthur J Hilliker, John P Phillips. Hum Mol Genet 2005
Peter R Anderson, Kim Kirby, Arthur J Hilliker, John P Phillips. Hum Mol Genet 2005
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Role of oxidative damage in Friedreich's ataxia.
J L Bradley, S Homayoun, P E Hart, A H V Schapira, J M Cooper. Neurochem Res 2004
J L Bradley, S Homayoun, P E Hart, A H V Schapira, J M Cooper. Neurochem Res 2004
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Inactivation of the Friedreich ataxia mouse gene leads to early embryonic lethality without iron accumulation.
M Cossée, H Puccio, A Gansmuller, H Koutnikova, A Dierich, M LeMeur, K Fischbeck, P Dollé, M Koenig. Hum Mol Genet 2000
M Cossée, H Puccio, A Gansmuller, H Koutnikova, A Dierich, M LeMeur, K Fischbeck, P Dollé, M Koenig. Hum Mol Genet 2000
13
Frataxin deficiency induces Schwann cell inflammation and death.
Chunye Lu, Robert Schoenfeld, Yuxi Shan, Hsing-Jo Tsai, Bruce Hammock, Gino Cortopassi. Biochim Biophys Acta 2009
Chunye Lu, Robert Schoenfeld, Yuxi Shan, Hsing-Jo Tsai, Bruce Hammock, Gino Cortopassi. Biochim Biophys Acta 2009
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Frataxin deficiency leads to reduced expression and impaired translocation of NF-E2-related factor (Nrf2) in cultured motor neurons.
Valentina D'Oria, Stefania Petrini, Lorena Travaglini, Chiara Priori, Emanuela Piermarini, Sara Petrillo, Barbara Carletti, Enrico Bertini, Fiorella Piemonte. Int J Mol Sci 2013
Valentina D'Oria, Stefania Petrini, Lorena Travaglini, Chiara Priori, Emanuela Piermarini, Sara Petrillo, Barbara Carletti, Enrico Bertini, Fiorella Piemonte. Int J Mol Sci 2013
22
Deletion of the yeast homologue of the human gene associated with Friedreich's ataxia elicits iron accumulation in mitochondria.
F Foury, O Cazzalini. FEBS Lett 1997
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Frataxin deficiency enhances apoptosis in cells differentiating into neuroectoderm.
M M Santos, K Ohshima, M Pandolfo. Hum Mol Genet 2001
M M Santos, K Ohshima, M Pandolfo. Hum Mol Genet 2001
21
Does oxidative stress contribute to the pathology of Friedreich's ataxia? A radical question.
Jeffrey S Armstrong, Omar Khdour, Sidney M Hecht. FASEB J 2010
Jeffrey S Armstrong, Omar Khdour, Sidney M Hecht. FASEB J 2010
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Reduction of Caenorhabditis elegans frataxin increases sensitivity to oxidative stress, reduces lifespan, and causes lethality in a mitochondrial complex II mutant.
Rafael P Vázquez-Manrique, Pilar González-Cabo, Sheila Ros, Homera Aziz, Howard A Baylis, Francesc Palau. FASEB J 2006
Rafael P Vázquez-Manrique, Pilar González-Cabo, Sheila Ros, Homera Aziz, Howard A Baylis, Francesc Palau. FASEB J 2006
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Frataxin acts as an iron chaperone protein to modulate mitochondrial aconitase activity.
Anne-Laure Bulteau, Heather A O'Neill, Mary Claire Kennedy, Masao Ikeda-Saito, Grazia Isaya, Luke I Szweda. Science 2004
Anne-Laure Bulteau, Heather A O'Neill, Mary Claire Kennedy, Masao Ikeda-Saito, Grazia Isaya, Luke I Szweda. Science 2004
11
Studies of human, mouse and yeast homologues indicate a mitochondrial function for frataxin.
H Koutnikova, V Campuzano, F Foury, P Dollé, O Cazzalini, M Koenig. Nat Genet 1997
H Koutnikova, V Campuzano, F Foury, P Dollé, O Cazzalini, M Koenig. Nat Genet 1997
11
Covalent binding of glutathione to hemoglobin. I. Inhibition of hemoglobin S polymerization.
M C Garel, C Domenget, J Caburi-Martin, C Prehu, F Galacteros, Y Beuzard. J Biol Chem 1986
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Increased glutathionylated hemoglobin (HbSSG) in type 2 diabetes subjects with microangiopathy.
Rangasamy Sampathkumar, Muthuswamy Balasubramanyam, Sadasivannair Sudarslal, Mohan Rema, Viswanthan Mohan, Padmanabhan Balaram. Clin Biochem 2005
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Iron-sulfur cluster biosynthesis. Characterization of frataxin as an iron donor for assembly of [2Fe-2S] clusters in ISU-type proteins.
Taejin Yoon, J A Cowan. J Am Chem Soc 2003
Taejin Yoon, J A Cowan. J Am Chem Soc 2003
11
S-glutathionylation: from redox regulation of protein functions to human diseases.
Daniela Giustarini, R Rossi, A Milzani, R Colombo, Isabella Dalle-Donne. J Cell Mol Med 2004
Daniela Giustarini, R Rossi, A Milzani, R Colombo, Isabella Dalle-Donne. J Cell Mol Med 2004
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Protein glutathionylation in erythrocytes.
Daniela Giustarini, Isabella Dalle-Donne, Roberto Colombo, Salvatore Petralia, Simonetta Giampaoletti, Aldo Milzani, Ranieri Rossi. Clin Chem 2003
Daniela Giustarini, Isabella Dalle-Donne, Roberto Colombo, Salvatore Petralia, Simonetta Giampaoletti, Aldo Milzani, Ranieri Rossi. Clin Chem 2003
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Functional genomic analysis of frataxin deficiency reveals tissue-specific alterations and identifies the PPARgamma pathway as a therapeutic target in Friedreich's ataxia.
Giovanni Coppola, Daniele Marmolino, Daning Lu, Qing Wang, Miriam Cnop, Myriam Rai, Fabio Acquaviva, Sergio Cocozza, Massimo Pandolfo, Daniel H Geschwind. Hum Mol Genet 2009
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12
Frataxin promotes antioxidant defense in a thiol-dependent manner resulting in diminished malignant transformation in vitro.
Sarah A Shoichet, Anselm T Bäumer, Djordje Stamenkovic, Heinrich Sauer, Andreas F H Pfeiffer, C Ronald Kahn, Dirk Müller-Wieland, Christoph Richter, Michael Ristow. Hum Mol Genet 2002
Sarah A Shoichet, Anselm T Bäumer, Djordje Stamenkovic, Heinrich Sauer, Andreas F H Pfeiffer, C Ronald Kahn, Dirk Müller-Wieland, Christoph Richter, Michael Ristow. Hum Mol Genet 2002
14
Co-cited is the co-citation frequency, indicating how many articles cite the article together with the query article. Similarity is the co-citation as percentage of the times cited of the query article or the article in the search results, whichever is the lowest. These numbers are calculated for the last 100 citations when articles are cited more than 100 times.