Anna Pastore, Giulia Tozzi, Laura Maria Gaeta, Enrico Bertini, Valentina Serafini, Silvia Di Cesare, Valentina Bonetto, Filippo Casoni, Rosalba Carrozzo, Giorgio Federici, Fiorella Piemonte. J Biol Chem 2003
Times Cited: 130
Times Cited: 130
Times Cited
Times Co-cited
Similarity
Impaired nuclear Nrf2 translocation undermines the oxidative stress response in Friedreich ataxia.
Vincent Paupe, Emmanuel P Dassa, Sergio Goncalves, Françoise Auchère, Maria Lönn, Arne Holmgren, Pierre Rustin. PLoS One 2009
Vincent Paupe, Emmanuel P Dassa, Sergio Goncalves, Françoise Auchère, Maria Lönn, Arne Holmgren, Pierre Rustin. PLoS One 2009
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Glutathione in blood of patients with Friedreich's ataxia.
F Piemonte, A Pastore, G Tozzi, D Tagliacozzi, F M Santorelli, R Carrozzo, C Casali, M Damiano, G Federici, E Bertini. Eur J Clin Invest 2001
F Piemonte, A Pastore, G Tozzi, D Tagliacozzi, F M Santorelli, R Carrozzo, C Casali, M Damiano, G Federici, E Bertini. Eur J Clin Invest 2001
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Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion.
V Campuzano, L Montermini, M D Moltò, L Pianese, M Cossée, F Cavalcanti, E Monros, F Rodius, F Duclos, A Monticelli,[...]. Science 1996
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Friedreich's ataxia: oxidative stress and cytoskeletal abnormalities.
Marco Sparaco, Laura Maria Gaeta, Filippo Maria Santorelli, Chiara Passarelli, Giulia Tozzi, Enrico Bertini, Alessandro Simonati, Francesco Scaravilli, Franco Taroni, Charles Duyckaerts,[...]. J Neurol Sci 2009
Marco Sparaco, Laura Maria Gaeta, Filippo Maria Santorelli, Chiara Passarelli, Giulia Tozzi, Enrico Bertini, Alessandro Simonati, Francesco Scaravilli, Franco Taroni, Charles Duyckaerts,[...]. J Neurol Sci 2009
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Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia.
A Rötig, P de Lonlay, D Chretien, F Foury, M Koenig, D Sidi, A Munnich, P Rustin. Nat Genet 1997
A Rötig, P de Lonlay, D Chretien, F Foury, M Koenig, D Sidi, A Munnich, P Rustin. Nat Genet 1997
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Reversible glutathionylation regulates actin polymerization in A431 cells.
J Wang, E S Boja, W Tan, E Tekle, H M Fales, S English, J J Mieyal, P B Chock. J Biol Chem 2001
J Wang, E S Boja, W Tan, E Tekle, H M Fales, S English, J J Mieyal, P B Chock. J Biol Chem 2001
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Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits.
H Puccio, D Simon, M Cossée, P Criqui-Filipe, F Tiziano, J Melki, C Hindelang, R Matyas, P Rustin, M Koenig. Nat Genet 2001
H Puccio, D Simon, M Cossée, P Criqui-Filipe, F Tiziano, J Melki, C Hindelang, R Matyas, P Rustin, M Koenig. Nat Genet 2001
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Identification by redox proteomics of glutathionylated proteins in oxidatively stressed human T lymphocytes.
Maddalena Fratelli, Hans Demol, Magda Puype, Simona Casagrande, Ivano Eberini, Mario Salmona, Valentina Bonetto, Manuela Mengozzi, Francis Duffieux, Emeric Miclet,[...]. Proc Natl Acad Sci U S A 2002
Maddalena Fratelli, Hans Demol, Magda Puype, Simona Casagrande, Ivano Eberini, Mario Salmona, Valentina Bonetto, Manuela Mengozzi, Francis Duffieux, Emeric Miclet,[...]. Proc Natl Acad Sci U S A 2002
22
The Friedreich's ataxia mutation confers cellular sensitivity to oxidant stress which is rescued by chelators of iron and calcium and inhibitors of apoptosis.
A Wong, J Yang, P Cavadini, C Gellera, B Lonnerdal, F Taroni, G Cortopassi. Hum Mol Genet 1999
A Wong, J Yang, P Cavadini, C Gellera, B Lonnerdal, F Taroni, G Cortopassi. Hum Mol Genet 1999
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Oxidative stress in patients with Friedreich ataxia.
J B Schulz, T Dehmer, L Schöls, H Mende, C Hardt, M Vorgerd, K Bürk, W Matson, J Dichgans, M F Beal,[...]. Neurology 2000
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Frataxin deficiency leads to defects in expression of antioxidants and Nrf2 expression in dorsal root ganglia of the Friedreich's ataxia YG8R mouse model.
Yuxi Shan, Robert A Schoenfeld, Genki Hayashi, Eleonora Napoli, Tasuku Akiyama, Mirela Iodi Carstens, Earl E Carstens, Mark A Pook, Gino A Cortopassi. Antioxid Redox Signal 2013
Yuxi Shan, Robert A Schoenfeld, Genki Hayashi, Eleonora Napoli, Tasuku Akiyama, Mirela Iodi Carstens, Earl E Carstens, Mark A Pook, Gino A Cortopassi. Antioxid Redox Signal 2013
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GAA repeat expansion mutation mouse models of Friedreich ataxia exhibit oxidative stress leading to progressive neuronal and cardiac pathology.
Sahar Al-Mahdawi, Ricardo Mouro Pinto, Dhaval Varshney, Lorraine Lawrence, Margaret B Lowrie, Sian Hughes, Zoe Webster, Julian Blake, J Mark Cooper, Rosalind King,[...]. Genomics 2006
Sahar Al-Mahdawi, Ricardo Mouro Pinto, Dhaval Varshney, Lorraine Lawrence, Margaret B Lowrie, Sian Hughes, Zoe Webster, Julian Blake, J Mark Cooper, Rosalind King,[...]. Genomics 2006
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Regulation of mitochondrial iron accumulation by Yfh1p, a putative homolog of frataxin.
M Babcock, D de Silva, R Oaks, S Davis-Kaplan, S Jiralerspong, L Montermini, M Pandolfo, J Kaplan. Science 1997
M Babcock, D de Silva, R Oaks, S Davis-Kaplan, S Jiralerspong, L Montermini, M Pandolfo, J Kaplan. Science 1997
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Glutathione-dependent redox status of frataxin-deficient cells in a yeast model of Friedreich's ataxia.
Françoise Auchère, Renata Santos, Sara Planamente, Emmanuel Lesuisse, Jean-Michel Camadro. Hum Mol Genet 2008
Françoise Auchère, Renata Santos, Sara Planamente, Emmanuel Lesuisse, Jean-Michel Camadro. Hum Mol Genet 2008
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Protein glutathionylation in human central nervous system: potential role in redox regulation of neuronal defense against free radicals.
Marco Sparaco, Laura Maria Gaeta, Giulia Tozzi, Enrico Bertini, Anna Pastore, Alessandro Simonati, Filippo Maria Santorelli, Fiorella Piemonte. J Neurosci Res 2006
Marco Sparaco, Laura Maria Gaeta, Giulia Tozzi, Enrico Bertini, Anna Pastore, Alessandro Simonati, Filippo Maria Santorelli, Fiorella Piemonte. J Neurosci Res 2006
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Disabled early recruitment of antioxidant defenses in Friedreich's ataxia.
K Chantrel-Groussard, V Geromel, H Puccio, M Koenig, A Munnich, A Rötig, P Rustin. Hum Mol Genet 2001
K Chantrel-Groussard, V Geromel, H Puccio, M Koenig, A Munnich, A Rötig, P Rustin. Hum Mol Genet 2001
18
Reversible S-glutathionylation of Cys 374 regulates actin filament formation by inducing structural changes in the actin molecule.
I Dalle-Donne, D Giustarini, R Rossi, R Colombo, A Milzani. Free Radic Biol Med 2003
I Dalle-Donne, D Giustarini, R Rossi, R Colombo, A Milzani. Free Radic Biol Med 2003
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Clinical, biochemical and molecular genetic correlations in Friedreich's ataxia.
J L Bradley, J C Blake, S Chamberlain, P K Thomas, J M Cooper, A H Schapira. Hum Mol Genet 2000
J L Bradley, J C Blake, S Chamberlain, P K Thomas, J M Cooper, A H Schapira. Hum Mol Genet 2000
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Increased levels of plasma malondialdehyde in Friedreich ataxia.
M Emond, G Lepage, M Vanasse, M Pandolfo. Neurology 2000
M Emond, G Lepage, M Vanasse, M Pandolfo. Neurology 2000
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Friedreich ataxia: molecular mechanisms, redox considerations, and therapeutic opportunities.
Renata Santos, Sophie Lefevre, Dominika Sliwa, Alexandra Seguin, Jean-Michel Camadro, Emmanuel Lesuisse. Antioxid Redox Signal 2010
Renata Santos, Sophie Lefevre, Dominika Sliwa, Alexandra Seguin, Jean-Michel Camadro, Emmanuel Lesuisse. Antioxid Redox Signal 2010
17
Frataxin is reduced in Friedreich ataxia patients and is associated with mitochondrial membranes.
V Campuzano, L Montermini, Y Lutz, L Cova, C Hindelang, S Jiralerspong, Y Trottier, S J Kish, B Faucheux, P Trouillas,[...]. Hum Mol Genet 1997
V Campuzano, L Montermini, Y Lutz, L Cova, C Hindelang, S Jiralerspong, Y Trottier, S J Kish, B Faucheux, P Trouillas,[...]. Hum Mol Genet 1997
15
Frataxin deficiency leads to reduced expression and impaired translocation of NF-E2-related factor (Nrf2) in cultured motor neurons.
Valentina D'Oria, Stefania Petrini, Lorena Travaglini, Chiara Priori, Emanuela Piermarini, Sara Petrillo, Barbara Carletti, Enrico Bertini, Fiorella Piemonte. Int J Mol Sci 2013
Valentina D'Oria, Stefania Petrini, Lorena Travaglini, Chiara Priori, Emanuela Piermarini, Sara Petrillo, Barbara Carletti, Enrico Bertini, Fiorella Piemonte. Int J Mol Sci 2013
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Clinical and genetic abnormalities in patients with Friedreich's ataxia.
A Dürr, M Cossee, Y Agid, V Campuzano, C Mignard, C Penet, J L Mandel, A Brice, M Koenig. N Engl J Med 1996
A Dürr, M Cossee, Y Agid, V Campuzano, C Mignard, C Penet, J L Mandel, A Brice, M Koenig. N Engl J Med 1996
14
Causative role of oxidative stress in a Drosophila model of Friedreich ataxia.
José V Llorens, Juan A Navarro, Maria J Martínez-Sebastián, Mary K Baylies, S Schneuwly, José A Botella, Maria D Moltó. FASEB J 2007
José V Llorens, Juan A Navarro, Maria J Martínez-Sebastián, Mary K Baylies, S Schneuwly, José A Botella, Maria D Moltó. FASEB J 2007
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Glutathionylation of the p50 subunit of NF-kappaB: a mechanism for redox-induced inhibition of DNA binding.
E Pineda-Molina, P Klatt, J Vázquez, A Marina, M García de Lacoba, D Pérez-Sala, S Lamas. Biochemistry 2001
E Pineda-Molina, P Klatt, J Vázquez, A Marina, M García de Lacoba, D Pérez-Sala, S Lamas. Biochemistry 2001
13
Frataxin-mediated iron delivery to ferrochelatase in the final step of heme biosynthesis.
Taejin Yoon, J A Cowan. J Biol Chem 2004
Taejin Yoon, J A Cowan. J Biol Chem 2004
13
Oxidative stress and protease dysfunction in the yeast model of Friedreich ataxia.
Anne-Laure Bulteau, Andrew Dancis, Monique Gareil, Jean-Jacques Montagne, Jean-Michel Camadro, Emmanuel Lesuisse. Free Radic Biol Med 2007
Anne-Laure Bulteau, Andrew Dancis, Monique Gareil, Jean-Jacques Montagne, Jean-Michel Camadro, Emmanuel Lesuisse. Free Radic Biol Med 2007
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Manganese superoxide dismutase induction by iron is impaired in Friedreich ataxia cells.
S Jiralerspong, B Ge, T J Hudson, M Pandolfo. FEBS Lett 2001
S Jiralerspong, B Ge, T J Hudson, M Pandolfo. FEBS Lett 2001
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Hydrogen peroxide scavenging rescues frataxin deficiency in a Drosophila model of Friedreich's ataxia.
Peter R Anderson, Kim Kirby, William C Orr, Arthur J Hilliker, John P Phillips. Proc Natl Acad Sci U S A 2008
Peter R Anderson, Kim Kirby, William C Orr, Arthur J Hilliker, John P Phillips. Proc Natl Acad Sci U S A 2008
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Antioxidant enzymes in blood of patients with Friedreich's ataxia.
G Tozzi, M Nuccetelli, M Lo Bello, S Bernardini, L Bellincampi, S Ballerini, L M Gaeta, C Casali, A Pastore, G Federici,[...]. Arch Dis Child 2002
G Tozzi, M Nuccetelli, M Lo Bello, S Bernardini, L Bellincampi, S Ballerini, L M Gaeta, C Casali, A Pastore, G Federici,[...]. Arch Dis Child 2002
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Regulation of protein function by S-glutathiolation in response to oxidative and nitrosative stress.
P Klatt, S Lamas. Eur J Biochem 2000
P Klatt, S Lamas. Eur J Biochem 2000
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A novel role for human sulfiredoxin in the reversal of glutathionylation.
Victoria J Findlay, Danyelle M Townsend, Taylor E Morris, Jacob P Fraser, Lin He, Kenneth D Tew. Cancer Res 2006
Victoria J Findlay, Danyelle M Townsend, Taylor E Morris, Jacob P Fraser, Lin He, Kenneth D Tew. Cancer Res 2006
12
An increase in S-glutathionylated proteins in the Alzheimer's disease inferior parietal lobule, a proteomics approach.
Shelley F Newman, Rukhsana Sultana, Marzia Perluigi, Rafella Coccia, Jian Cai, William M Pierce, Jon B Klein, Delano M Turner, D Allan Butterfield. J Neurosci Res 2007
Shelley F Newman, Rukhsana Sultana, Marzia Perluigi, Rafella Coccia, Jian Cai, William M Pierce, Jon B Klein, Delano M Turner, D Allan Butterfield. J Neurosci Res 2007
12
S-glutathionylation: from redox regulation of protein functions to human diseases.
Daniela Giustarini, R Rossi, A Milzani, R Colombo, Isabella Dalle-Donne. J Cell Mol Med 2004
Daniela Giustarini, R Rossi, A Milzani, R Colombo, Isabella Dalle-Donne. J Cell Mol Med 2004
12
Reduction of Caenorhabditis elegans frataxin increases sensitivity to oxidative stress, reduces lifespan, and causes lethality in a mitochondrial complex II mutant.
Rafael P Vázquez-Manrique, Pilar González-Cabo, Sheila Ros, Homera Aziz, Howard A Baylis, Francesc Palau. FASEB J 2006
Rafael P Vázquez-Manrique, Pilar González-Cabo, Sheila Ros, Homera Aziz, Howard A Baylis, Francesc Palau. FASEB J 2006
16
The dorsal root ganglion in Friedreich's ataxia.
Arnulf H Koeppen, Jennifer A Morral, Ashley N Davis, Jiang Qian, Simone V Petrocine, Mitchell D Knutson, Walter M Gibson, Matthew J Cusack, Danhong Li. Acta Neuropathol 2009
Arnulf H Koeppen, Jennifer A Morral, Ashley N Davis, Jiang Qian, Simone V Petrocine, Mitchell D Knutson, Walter M Gibson, Matthew J Cusack, Danhong Li. Acta Neuropathol 2009
14
Molecular mechanisms and clinical implications of reversible protein S-glutathionylation.
John J Mieyal, Molly M Gallogly, Suparna Qanungo, Elizabeth A Sabens, Melissa D Shelton. Antioxid Redox Signal 2008
John J Mieyal, Molly M Gallogly, Suparna Qanungo, Elizabeth A Sabens, Melissa D Shelton. Antioxid Redox Signal 2008
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Stable and controllable RNA interference: Investigating the physiological function of glutathionylated actin.
Jun Wang, Ephrem Tekle, Hammou Oubrahim, John J Mieyal, Earl R Stadtman, P Boon Chock. Proc Natl Acad Sci U S A 2003
Jun Wang, Ephrem Tekle, Hammou Oubrahim, John J Mieyal, Earl R Stadtman, P Boon Chock. Proc Natl Acad Sci U S A 2003
12
Friedreich's ataxia: pathology, pathogenesis, and molecular genetics.
Arnulf H Koeppen. J Neurol Sci 2011
Arnulf H Koeppen. J Neurol Sci 2011
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Iron-sulfur cluster synthesis, iron homeostasis and oxidative stress in Friedreich ataxia.
Rachael A Vaubel, Grazia Isaya. Mol Cell Neurosci 2013
Rachael A Vaubel, Grazia Isaya. Mol Cell Neurosci 2013
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Redox environment of the cell as viewed through the redox state of the glutathione disulfide/glutathione couple.
F Q Schafer, G R Buettner. Free Radic Biol Med 2001
F Q Schafer, G R Buettner. Free Radic Biol Med 2001
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Identification of S-glutathionylated cellular proteins during oxidative stress and constitutive metabolism by affinity purification and proteomic analysis.
Christina Lind, Robert Gerdes, Ylva Hamnell, Ina Schuppe-Koistinen, Helena Brockenhuus von Löwenhielm, Arne Holmgren, Ian A Cotgreave. Arch Biochem Biophys 2002
Christina Lind, Robert Gerdes, Ylva Hamnell, Ina Schuppe-Koistinen, Helena Brockenhuus von Löwenhielm, Arne Holmgren, Ian A Cotgreave. Arch Biochem Biophys 2002
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Actin S-glutathionylation: evidence against a thiol-disulphide exchange mechanism.
Isabella Dalle-Donne, Ranieri Rossi, Daniela Giustarini, Roberto Colombo, Aldo Milzani. Free Radic Biol Med 2003
Isabella Dalle-Donne, Ranieri Rossi, Daniela Giustarini, Roberto Colombo, Aldo Milzani. Free Radic Biol Med 2003
11
Glutaredoxin 2 catalyzes the reversible oxidation and glutathionylation of mitochondrial membrane thiol proteins: implications for mitochondrial redox regulation and antioxidant DEFENSE.
Samantha M Beer, Ellen R Taylor, Stephanie E Brown, Christina C Dahm, Nikola J Costa, Michael J Runswick, Michael P Murphy. J Biol Chem 2004
Samantha M Beer, Ellen R Taylor, Stephanie E Brown, Christina C Dahm, Nikola J Costa, Michael J Runswick, Michael P Murphy. J Biol Chem 2004
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Friedreich ataxia: the oxidative stress paradox.
Hervé Seznec, Delphine Simon, Cécile Bouton, Laurence Reutenauer, Ariane Hertzog, Pawel Golik, Vincent Procaccio, Manisha Patel, Jean-Claude Drapier, Michel Koenig,[...]. Hum Mol Genet 2005
Hervé Seznec, Delphine Simon, Cécile Bouton, Laurence Reutenauer, Ariane Hertzog, Pawel Golik, Vincent Procaccio, Manisha Patel, Jean-Claude Drapier, Michel Koenig,[...]. Hum Mol Genet 2005
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Decline of contractility during ischemia-reperfusion injury: actin glutathionylation and its effect on allosteric interaction with tropomyosin.
Frank C Chen, Ozgur Ogut. Am J Physiol Cell Physiol 2006
Frank C Chen, Ozgur Ogut. Am J Physiol Cell Physiol 2006
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Dynamic redox control of NF-kappaB through glutaredoxin-regulated S-glutathionylation of inhibitory kappaB kinase beta.
Niki L Reynaert, Albert van der Vliet, Amy S Guala, Toby McGovern, Milena Hristova, Cristen Pantano, Nicholas H Heintz, John Heim, Ye-Shih Ho, Dwight E Matthews,[...]. Proc Natl Acad Sci U S A 2006
Niki L Reynaert, Albert van der Vliet, Amy S Guala, Toby McGovern, Milena Hristova, Cristen Pantano, Nicholas H Heintz, John Heim, Ye-Shih Ho, Dwight E Matthews,[...]. Proc Natl Acad Sci U S A 2006
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Protein oxidation in the brain in Alzheimer's disease.
M Y Aksenov, M V Aksenova, D A Butterfield, J W Geddes, W R Markesbery. Neuroscience 2001
M Y Aksenov, M V Aksenova, D A Butterfield, J W Geddes, W R Markesbery. Neuroscience 2001
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Mechanisms of reversible protein glutathionylation in redox signaling and oxidative stress.
Molly M Gallogly, John J Mieyal. Curr Opin Pharmacol 2007
Molly M Gallogly, John J Mieyal. Curr Opin Pharmacol 2007
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An interaction between frataxin and Isu1/Nfs1 that is crucial for Fe/S cluster synthesis on Isu1.
Jana Gerber, Ulrich Mühlenhoff, Roland Lill. EMBO Rep 2003
Jana Gerber, Ulrich Mühlenhoff, Roland Lill. EMBO Rep 2003
10
Co-cited is the co-citation frequency, indicating how many articles cite the article together with the query article. Similarity is the co-citation as percentage of the times cited of the query article or the article in the search results, whichever is the lowest. These numbers are calculated for the last 100 citations when articles are cited more than 100 times.