Nathalie Boddaert, Kim Hanh Le Quan Sang, Agnès Rötig, Anne Leroy-Willig, Serge Gallet, Francis Brunelle, Daniel Sidi, Jean-Christophe Thalabard, Arnold Munnich, Z Ioav Cabantchik. Blood 2007
Times Cited: 291
Times Cited: 291
Times Cited
Times Co-cited
Similarity
Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion.
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Targeting chelatable iron as a therapeutic modality in Parkinson's disease.
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Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits.
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The dentate nucleus in Friedreich's ataxia: the role of iron-responsive proteins.
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Metal-protein attenuation with iodochlorhydroxyquin (clioquinol) targeting Abeta amyloid deposition and toxicity in Alzheimer disease: a pilot phase 2 clinical trial.
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Iron-export ferroxidase activity of β-amyloid precursor protein is inhibited by zinc in Alzheimer's disease.
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The Friedreich's ataxia mutation confers cellular sensitivity to oxidant stress which is rescued by chelators of iron and calcium and inhibitors of apoptosis.
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Identification of nonferritin mitochondrial iron deposits in a mouse model of Friedreich ataxia.
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Iron-dependent regulation of frataxin expression: implications for treatment of Friedreich ataxia.
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Relation of cytosolic iron excess to cardiomyopathy of Friedreich's ataxia.
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Iron-sulfur cluster synthesis, iron homeostasis and oxidative stress in Friedreich ataxia.
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The MCK mouse heart model of Friedreich's ataxia: Alterations in iron-regulated proteins and cardiac hypertrophy are limited by iron chelation.
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Iron promotes the toxicity of amyloid beta peptide by impeding its ordered aggregation.
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Co-cited is the co-citation frequency, indicating how many articles cite the article together with the query article. Similarity is the co-citation as percentage of the times cited of the query article or the article in the search results, whichever is the lowest. These numbers are calculated for the last 100 citations when articles are cited more than 100 times.