A citation-based method for searching scientific literature

Judit M Pérez Ortiz, Harry T Orr. Adv Exp Med Biol 2018
Times Cited: 13







List of co-cited articles
54 articles co-cited >1



Times Cited
  Times     Co-cited
Similarity


Spinocerebellar ataxia.
Thomas Klockgether, Caterina Mariotti, Henry L Paulson. Nat Rev Dis Primers 2019
136
30

SCA1 transgenic mice: a model for neurodegeneration caused by an expanded CAG trinucleotide repeat.
E N Burright, H B Clark, A Servadio, T Matilla, R M Feddersen, W S Yunis, L A Duvick, H Y Zoghbi, H T Orr. Cell 1995
461
23

Ataxin-1 nuclear localization and aggregation: role in polyglutamine-induced disease in SCA1 transgenic mice.
I A Klement, P J Skinner, M D Kaytor, H Yi, S M Hersch, H B Clark, H Y Zoghbi, H T Orr. Cell 1998
799
23


CAG expansions in a novel gene for Machado-Joseph disease at chromosome 14q32.1.
Y Kawaguchi, T Okamoto, M Taniwaki, M Aizawa, M Inoue, S Katayama, H Kawakami, S Nakamura, M Nishimura, I Akiguchi. Nat Genet 1994
23

Expansion of an unstable trinucleotide CAG repeat in spinocerebellar ataxia type 1.
H T Orr, M Y Chung, S Banfi, T J Kwiatkowski, A Servadio, A L Beaudet, A E McCall, L A Duvick, L P Ranum, H Y Zoghbi. Nat Genet 1993
23

Partial loss of ataxin-1 function contributes to transcriptional dysregulation in spinocerebellar ataxia type 1 pathogenesis.
Juan Crespo-Barreto, John D Fryer, Chad A Shaw, Harry T Orr, Huda Y Zoghbi. PLoS Genet 2010
85
15

ATAXIN-1 interacts with the repressor Capicua in its native complex to cause SCA1 neuropathology.
Yung C Lam, Aaron B Bowman, Paymaan Jafar-Nejad, Janghoo Lim, Ronald Richman, John D Fryer, Eric D Hyun, Lisa A Duvick, Harry T Orr, Juan Botas,[...]. Cell 2006
210
15

Exercise and genetic rescue of SCA1 via the transcriptional repressor Capicua.
John D Fryer, Peng Yu, Hyojin Kang, Caleigh Mandel-Brehm, Angela N Carter, Juan Crespo-Barreto, Yan Gao, Adriano Flora, Chad Shaw, Harry T Orr,[...]. Science 2011
95
15

Trinucleotide repeat disorders.
Harry T Orr, Huda Y Zoghbi. Annu Rev Neurosci 2007
972
15

Nonallele specific silencing of ataxin-7 improves disease phenotypes in a mouse model of SCA7.
Pavitra S Ramachandran, Ryan L Boudreau, Kellie A Schaefer, Albert R La Spada, Beverly L Davidson. Mol Ther 2014
37
15

Neurologic findings in Machado-Joseph disease: relation with disease duration, subtypes, and (CAG)n.
L B Jardim, M L Pereira, I Silveira, A Ferro, J Sequeiros, R Giugliani. Arch Neurol 2001
105
15

Peripheral androgen receptor gene suppression rescues disease in mouse models of spinal and bulbar muscular atrophy.
Andrew P Lieberman, Zhigang Yu, Sue Murray, Raechel Peralta, Audrey Low, Shuling Guo, Xing Xian Yu, Constanza J Cortes, C Frank Bennett, Brett P Monia,[...]. Cell Rep 2014
111
15

Spinocerebellar ataxia 3 and Machado-Joseph disease: clinical, molecular, and neuropathological features.
A Dürr, G Stevanin, G Cancel, C Duyckaerts, N Abbas, O Didierjean, H Chneiweiss, A Benomar, O Lyon-Caen, J Julien,[...]. Ann Neurol 1996
337
15

Riluzole in patients with hereditary cerebellar ataxia: a randomised, double-blind, placebo-controlled trial.
Silvia Romano, Giulia Coarelli, Christian Marcotulli, Luca Leonardi, Francesca Piccolo, Maria Spadaro, Marina Frontali, Michela Ferraldeschi, Maria Chiara Vulpiani, Federica Ponzelli,[...]. Lancet Neurol 2015
100
15

Allele-selective inhibition of mutant atrophin-1 expression by duplex and single-stranded RNAs.
Jiaxin Hu, Jing Liu, K Jayaprakash Narayanannair, Jeremy G Lackey, Satya Kuchimanchi, Kallanthottathil G Rajeev, Muthiah Manoharan, Eric E Swayze, Walt F Lima, Thazha P Prakash,[...]. Biochemistry 2014
24
15

A neurological disease caused by an expanded CAG trinucleotide repeat in the TATA-binding protein gene: a new polyglutamine disease?
R Koide, S Kobayashi, T Shimohata, T Ikeuchi, M Maruyama, M Saito, M Yamada, H Takahashi, S Tsuji. Hum Mol Genet 1999
278
15

Spinocerebellar ataxia type 6: gaze-evoked and vertical nystagmus, Purkinje cell degeneration, and variable age of onset.
C M Gomez, R M Thompson, J T Gammack, S L Perlman, W B Dobyns, C L Truwit, D S Zee, H B Clark, J H Anderson. Ann Neurol 1997
202
15

Brain pathology of spinocerebellar ataxias.
Kay Seidel, Sonny Siswanto, Ewout R P Brunt, Wilfred den Dunnen, Horst-Werner Korf, Udo Rüb. Acta Neuropathol 2012
214
15

Oligonucleotide therapy mitigates disease in spinocerebellar ataxia type 3 mice.
Hayley S McLoughlin, Lauren R Moore, Ravi Chopra, Robert Komlo, Megan McKenzie, Kate G Blumenstein, Hien Zhao, Holly B Kordasiewicz, Vikram G Shakkottai, Henry L Paulson. Ann Neurol 2018
67
15

ATXN1-CIC Complex Is the Primary Driver of Cerebellar Pathology in Spinocerebellar Ataxia Type 1 through a Gain-of-Function Mechanism.
Maxime W C Rousseaux, Tyler Tschumperlin, Hsiang-Chih Lu, Elizabeth P Lackey, Vitaliy V Bondar, Ying-Wooi Wan, Qiumin Tan, Carolyn J Adamski, Jillian Friedrich, Kirk Twaroski,[...]. Neuron 2018
38
15

Molecular pathogenesis of spinocerebellar ataxia type 1 disease.
Seongman Kang, Sunghoi Hong. Mol Cells 2009
21
15

Serine 776 of ataxin-1 is critical for polyglutamine-induced disease in SCA1 transgenic mice.
Effat S Emamian, Michael D Kaytor, Lisa A Duvick, Tao Zu, Susan K Tousey, Huda Y Zoghbi, H Brent Clark, Harry T Orr. Neuron 2003
223
15

Machado-Joseph disease/spinocerebellar ataxia type 3.
Henry Paulson. Handb Clin Neurol 2012
80
15

The deubiquitinating enzyme ataxin-3, a polyglutamine disease protein, edits Lys63 linkages in mixed linkage ubiquitin chains.
Brett J Winborn, Sue M Travis, Sokol V Todi, K Matthew Scaglione, Ping Xu, Aislinn J Williams, Robert E Cohen, Junmin Peng, Henry L Paulson. J Biol Chem 2008
182
15

Construction of transgenic Drosophila by using the site-specific integrase from phage phiC31.
Amy C Groth, Matthew Fish, Roel Nusse, Michele P Calos. Genetics 2004
703
15

Polyglutamine Repeats in Neurodegenerative Diseases.
Andrew P Lieberman, Vikram G Shakkottai, Roger L Albin. Annu Rev Pathol 2019
75
15

Understanding the role of the Josephin domain in the PolyUb binding and cleavage properties of ataxin-3.
Giuseppe Nicastro, Sokol V Todi, Ezgi Karaca, Alexandre M J J Bonvin, Henry L Paulson, Annalisa Pastore. PLoS One 2010
47
15



The two-stage pathway of ataxin-3 fibrillogenesis involves a polyglutamine-independent step.
Andrew M Ellisdon, Bronwen Thomas, Stephen P Bottomley. J Biol Chem 2006
135
15


Endurance exercise and selective breeding for longevity extend Drosophila healthspan by overlapping mechanisms.
Alyson Sujkowski, Brian Bazzell, Kylie Carpenter, Robert Arking, Robert J Wessells. Aging (Albany NY) 2015
37
15

The deubiquitinase ataxin-3 requires Rad23 and DnaJ-1 for its neuroprotective role in Drosophila melanogaster.
Wei-Ling Tsou, Michelle Ouyang, Ryan R Hosking, Joanna R Sutton, Jessica R Blount, Aaron A Burr, Sokol V Todi. Neurobiol Dis 2015
30
15

Josephin domain of ataxin-3 contains two distinct ubiquitin-binding sites.
Giuseppe Nicastro, Laura Masino, Veronica Esposito, Rajesh P Menon, Alfonso De Simone, Franca Fraternali, Annalisa Pastore. Biopolymers 2009
63
15

Toward understanding Machado-Joseph disease.
Maria do Carmo Costa, Henry L Paulson. Prog Neurobiol 2012
158
15

An arginine/lysine-rich motif is crucial for VCP/p97-mediated modulation of ataxin-3 fibrillogenesis.
Annett Boeddrich, Sébastien Gaumer, Annette Haacke, Nikolay Tzvetkov, Mario Albrecht, Bernd O Evert, Eva C Müller, Rudi Lurz, Peter Breuer, Nancy Schugardt,[...]. EMBO J 2006
122
15

Ubiquitination directly enhances activity of the deubiquitinating enzyme ataxin-3.
Sokol V Todi, Brett J Winborn, K Matthew Scaglione, Jessica R Blount, Sue M Travis, Henry L Paulson. EMBO J 2009
121
15

The Josephin domain determines the morphological and mechanical properties of ataxin-3 fibrils.
Laura Masino, Giuseppe Nicastro, Alfonso De Simone, Lesley Calder, Justin Molloy, Annalisa Pastore. Biophys J 2011
39
15

Characterization of the structure and the amyloidogenic properties of the Josephin domain of the polyglutamine-containing protein ataxin-3.
Laura Masino, Giuseppe Nicastro, Rajesh P Menon, Fabrizio Dal Piaz, Lesley Calder, Annalisa Pastore. J Mol Biol 2004
98
15

Expression and Regulation of Deubiquitinase-Resistant, Unanchored Ubiquitin Chains in Drosophila.
Jessica R Blount, Kozeta Libohova, Gregory B Marsh, Joanna R Sutton, Sokol V Todi. Sci Rep 2018
7
28

Ubiquitination regulates the neuroprotective function of the deubiquitinase ataxin-3 in vivo.
Wei-Ling Tsou, Aaron A Burr, Michelle Ouyang, Jessica R Blount, K Matthew Scaglione, Sokol V Todi. J Biol Chem 2013
32
15

Polyglutamine length-dependent toxicity from α1ACT in Drosophila models of spinocerebellar ataxia type 6.
Wei-Ling Tsou, Sultan H Qiblawi, Ryan R Hosking, Christopher M Gomez, Sokol V Todi. Biol Open 2016
12
16

Interaction of the polyglutamine protein ataxin-3 with Rad23 regulates toxicity in Drosophila models of Spinocerebellar Ataxia Type 3.
Joanna R Sutton, Jessica R Blount, Kozeta Libohova, Wei-Ling Tsou, Gnanada S Joshi, Henry L Paulson, Maria do Carmo Costa, K Matthew Scaglione, Sokol V Todi. Hum Mol Genet 2017
21
15

Differential toxicity of ataxin-3 isoforms in Drosophila models of Spinocerebellar Ataxia Type 3.
Sean L Johnson, Jessica R Blount, Kozeta Libohova, Bedri Ranxhi, Henry L Paulson, Wei-Ling Tsou, Sokol V Todi. Neurobiol Dis 2019
8
25

Splice isoforms of the polyglutamine disease protein ataxin-3 exhibit similar enzymatic yet different aggregation properties.
Ginny Marie Harris, Katerina Dodelzon, Lijie Gong, Pedro Gonzalez-Alegre, Henry L Paulson. PLoS One 2010
44
15

DnaJ-1 and karyopherin α3 suppress degeneration in a new Drosophila model of Spinocerebellar Ataxia Type 6.
Wei-Ling Tsou, Ryan R Hosking, Aaron A Burr, Joanna R Sutton, Michelle Ouyang, Xiaofei Du, Christopher M Gomez, Sokol V Todi. Hum Mol Genet 2015
26
15

Defining the role of ubiquitin-interacting motifs in the polyglutamine disease protein, ataxin-3.
Sarah J Shoesmith Berke, Yaohui Chai, Ginger L Marrs, Hsiang Wen, Henry L Paulson. J Biol Chem 2005
75
15

Cellular turnover of the polyglutamine disease protein ataxin-3 is regulated by its catalytic activity.
Sokol V Todi, Mario N Laco, Brett J Winborn, Sue M Travis, Hsiang M Wen, Henry L Paulson. J Biol Chem 2007
37
15

Ubiquitin-binding site 2 of ataxin-3 prevents its proteasomal degradation by interacting with Rad23.
Jessica R Blount, Wei-Ling Tsou, Gorica Ristic, Aaron A Burr, Michelle Ouyang, Holland Galante, K Matthew Scaglione, Sokol V Todi. Nat Commun 2014
42
15


Co-cited is the co-citation frequency, indicating how many articles cite the article together with the query article. Similarity is the co-citation as percentage of the times cited of the query article or the article in the search results, whichever is the lowest. These numbers are calculated for the last 100 citations when articles are cited more than 100 times.