Evelina Valionyte, Yi Yang, Sheridan L Roberts, Jack Kelly, Boxun Lu, Shouqing Luo. J Mol Biol 2020
Times Cited: 20
Times Cited: 20
Times Cited
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Similarity
Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain.
M DiFiglia, E Sapp, K O Chase, S W Davies, G P Bates, J P Vonsattel, N Aronin. Science 1997
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Potential function for the Huntingtin protein as a scaffold for selective autophagy.
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Cargo recognition failure is responsible for inefficient autophagy in Huntington's disease.
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Huntingtin functions as a scaffold for selective macroautophagy.
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Epigenetics of Huntington's Disease.
Silvia Bassi, Takshashila Tripathi, Alan Monziani, Francesca Di Leva, Marta Biagioli. Adv Exp Med Biol 2017
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A role for autophagy in Huntington's disease.
Katherine R Croce, Ai Yamamoto. Neurobiol Dis 2019
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Huntingtin controls neurotrophic support and survival of neurons by enhancing BDNF vesicular transport along microtubules.
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Inhibition of mTOR induces autophagy and reduces toxicity of polyglutamine expansions in fly and mouse models of Huntington disease.
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alpha-Synuclein locus triplication causes Parkinson's disease.
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Huntington's disease: from molecular pathogenesis to clinical treatment.
Christopher A Ross, Sarah J Tabrizi. Lancet Neurol 2011
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Huntington's Disease and Mitochondria.
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The pathobiology of perturbed mutant huntingtin protein-protein interactions in Huntington's disease.
Erich E Wanker, Anne Ast, Franziska Schindler, Philipp Trepte, Sigrid Schnoegl. J Neurochem 2019
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PGC-1α, mitochondrial dysfunction, and Huntington's disease.
Ashu Johri, Abhishek Chandra, M Flint Beal. Free Radic Biol Med 2013
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Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation.
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The cryo-electron microscopy structure of huntingtin.
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Proteostasis in Huntington's disease: disease mechanisms and therapeutic opportunities.
Rachel J Harding, Yu-Feng Tong. Acta Pharmacol Sin 2018
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AMPK activation protects from neuronal dysfunction and vulnerability across nematode, cellular and mouse models of Huntington's disease.
Rafael P Vázquez-Manrique, Francesca Farina, Karine Cambon, María Dolores Sequedo, Alex J Parker, José María Millán, Andreas Weiss, Nicole Déglon, Christian Neri. Hum Mol Genet 2016
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Huntington's Disease-Update on Treatments.
Kara J Wyant, Andrew J Ridder, Praveen Dayalu. Curr Neurol Neurosci Rep 2017
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Targeting the proteostasis network in Huntington's disease.
Tânia R Soares, Sara D Reis, Brígida R Pinho, Michael R Duchen, Jorge M A Oliveira. Ageing Res Rev 2019
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Huntingtin-Lowering Therapies for Huntington Disease: A Review of the Evidence of Potential Benefits and Risks.
Blair R Leavitt, Holly B Kordasiewicz, Scott A Schobel. JAMA Neurol 2020
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Molecular Pathogenesis in Huntington's Disease.
S N Illarioshkin, S A Klyushnikov, V A Vigont, Yu A Seliverstov, E V Kaznacheyeva. Biochemistry (Mosc) 2018
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Protein Misfolding and ER Stress in Huntington's Disease.
Talya Shacham, Neeraj Sharma, Gerardo Z Lederkremer. Front Mol Biosci 2019
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IRE1 plays an essential role in ER stress-mediated aggregation of mutant huntingtin via the inhibition of autophagy flux.
Huikyong Lee, Jee-Yeon Noh, Yumin Oh, Youngdoo Kim, Jae-Woong Chang, Chul-Woong Chung, Soon-Tae Lee, Manho Kim, Hoon Ryu, Yong-Keun Jung. Hum Mol Genet 2012
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Prion-like transmission of protein aggregates in neurodegenerative diseases.
Patrik Brundin, Ronald Melki, Ron Kopito. Nat Rev Mol Cell Biol 2010
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Disruption of axonal transport by loss of huntingtin or expression of pathogenic polyQ proteins in Drosophila.
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Altered Regulation of Striatal Neuronal N-Methyl-D-Aspartate Receptor Trafficking by Palmitoylation in Huntington Disease Mouse Model.
Rujun Kang, Liang Wang, Shaun S Sanders, Kurt Zuo, Michael R Hayden, Lynn A Raymond. Front Synaptic Neurosci 2019
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Amelioration of Huntington's disease phenotypes by Beta-Lapachone is associated with increases in Sirt1 expression, CREB phosphorylation and PGC-1α deacetylation.
Mijung Lee, Jae-Jun Ban, Jin-Young Chung, Wooseok Im, Manho Kim. PLoS One 2018
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15
Ganglioside GM1 induces phosphorylation of mutant huntingtin and restores normal motor behavior in Huntington disease mice.
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Histone deacetylase 6 inhibition compensates for the transport deficit in Huntington's disease by increasing tubulin acetylation.
Jim P Dompierre, Juliette D Godin, Bénédicte C Charrin, Fabrice P Cordelières, Stephen J King, Sandrine Humbert, Frédéric Saudou. J Neurosci 2007
Jim P Dompierre, Juliette D Godin, Bénédicte C Charrin, Fabrice P Cordelières, Stephen J King, Sandrine Humbert, Frédéric Saudou. J Neurosci 2007
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Drp1 phosphorylation by MAPK1 causes mitochondrial dysfunction in cell culture model of Huntington's disease.
Anne Jessica Roe, Xin Qi. Biochem Biophys Res Commun 2018
Anne Jessica Roe, Xin Qi. Biochem Biophys Res Commun 2018
15
Mutant huntingtin binds the mitochondrial fission GTPase dynamin-related protein-1 and increases its enzymatic activity.
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Huntingtin phosphorylation acts as a molecular switch for anterograde/retrograde transport in neurons.
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Acetylation targets mutant huntingtin to autophagosomes for degradation.
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VCP recruitment to mitochondria causes mitophagy impairment and neurodegeneration in models of Huntington's disease.
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MAP kinase phosphatase 1 (MKP-1/DUSP1) is neuroprotective in Huntington's disease via additive effects of JNK and p38 inhibition.
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IKK phosphorylates Huntingtin and targets it for degradation by the proteasome and lysosome.
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Ubiquitin-proteasome system involvement in Huntington's disease.
Zaira Ortega, Jose J Lucas. Front Mol Neurosci 2014
Zaira Ortega, Jose J Lucas. Front Mol Neurosci 2014
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Polyglutamine pathogenesis: emergence of unifying mechanisms for Huntington's disease and related disorders.
Christopher A Ross. Neuron 2002
Christopher A Ross. Neuron 2002
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Dopamine-modified alpha-synuclein blocks chaperone-mediated autophagy.
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Constitutive upregulation of chaperone-mediated autophagy in Huntington's disease.
Hiroshi Koga, Marta Martinez-Vicente, Esperanza Arias, Susmita Kaushik, David Sulzer, Ana Maria Cuervo. J Neurosci 2011
Hiroshi Koga, Marta Martinez-Vicente, Esperanza Arias, Susmita Kaushik, David Sulzer, Ana Maria Cuervo. J Neurosci 2011
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The many faces of autophagy dysfunction in Huntington's disease: from mechanism to therapy.
Constanza J Cortes, Albert R La Spada. Drug Discov Today 2014
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Protein misfolding, aggregation, and conformational strains in neurodegenerative diseases.
Claudio Soto, Sandra Pritzkow. Nat Neurosci 2018
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Aggregate-prone proteins with polyglutamine and polyalanine expansions are degraded by autophagy.
Brinda Ravikumar, Rainer Duden, David C Rubinsztein. Hum Mol Genet 2002
Brinda Ravikumar, Rainer Duden, David C Rubinsztein. Hum Mol Genet 2002
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Trehalose alleviates polyglutamine-mediated pathology in a mouse model of Huntington disease.
Motomasa Tanaka, Yoko Machida, Sanyong Niu, Tetsurou Ikeda, Nihar R Jana, Hiroshi Doi, Masaru Kurosawa, Munenori Nekooki, Nobuyuki Nukina. Nat Med 2004
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Mutant HTT (huntingtin) impairs mitophagy in a cellular model of Huntington disease.
Sandra Franco-Iborra, Ainhoa Plaza-Zabala, Marta Montpeyo, David Sebastian, Miquel Vila, Marta Martinez-Vicente. Autophagy 2021
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Huntington disease.
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Metformin treatment reduces motor and neuropsychiatric phenotypes in the zQ175 mouse model of Huntington disease.
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Role of brain-derived neurotrophic factor in Huntington's disease.
Chiara Zuccato, Elena Cattaneo. Prog Neurobiol 2007
Chiara Zuccato, Elena Cattaneo. Prog Neurobiol 2007
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Co-cited is the co-citation frequency, indicating how many articles cite the article together with the query article. Similarity is the co-citation as percentage of the times cited of the query article or the article in the search results, whichever is the lowest. These numbers are calculated for the last 100 citations when articles are cited more than 100 times.