Justin J Yerbury, Natalie E Farrawell, Luke McAlary. Trends Neurosci 2020
Times Cited: 22
Times Cited: 22
Times Cited
Times Co-cited
Similarity
Ubiquitinated TDP-43 in frontotemporal lobar degeneration and amyotrophic lateral sclerosis.
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40
Spinal motor neuron protein supersaturation patterns are associated with inclusion body formation in ALS.
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State of play in amyotrophic lateral sclerosis genetics.
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Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis.
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SOD1A4V aggregation alters ubiquitin homeostasis in a cell model of ALS.
Natalie E Farrawell, Isabella Lambert-Smith, Kristen Mitchell, Jessie McKenna, Luke McAlary, Prajwal Ciryam, Kara L Vine, Darren N Saunders, Justin J Yerbury. J Cell Sci 2018
Natalie E Farrawell, Isabella Lambert-Smith, Kristen Mitchell, Jessie McKenna, Luke McAlary, Prajwal Ciryam, Kara L Vine, Darren N Saunders, Justin J Yerbury. J Cell Sci 2018
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ALS Genetics, Mechanisms, and Therapeutics: Where Are We Now?
Rita Mejzini, Loren L Flynn, Ianthe L Pitout, Sue Fletcher, Steve D Wilton, P Anthony Akkari. Front Neurosci 2019
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Converging mechanisms in ALS and FTD: disrupted RNA and protein homeostasis.
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Decoding ALS: from genes to mechanism.
J Paul Taylor, Robert H Brown, Don W Cleveland. Nature 2016
J Paul Taylor, Robert H Brown, Don W Cleveland. Nature 2016
22
Exome sequencing in amyotrophic lateral sclerosis identifies risk genes and pathways.
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22
TDP-43 pathology and neuronal loss in amyotrophic lateral sclerosis spinal cord.
Johannes Brettschneider, Kimihito Arai, Kelly Del Tredici, Jon B Toledo, John L Robinson, Edward B Lee, Satoshi Kuwabara, Kazumoto Shibuya, David J Irwin, Lubin Fang,[...]. Acta Neuropathol 2014
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22
Targeted gene expression as a means of altering cell fates and generating dominant phenotypes.
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Amyotrophic lateral sclerosis.
Orla Hardiman, Ammar Al-Chalabi, Adriano Chio, Emma M Corr, Giancarlo Logroscino, Wim Robberecht, Pamela J Shaw, Zachary Simmons, Leonard H van den Berg. Nat Rev Dis Primers 2017
Orla Hardiman, Ammar Al-Chalabi, Adriano Chio, Emma M Corr, Giancarlo Logroscino, Wim Robberecht, Pamela J Shaw, Zachary Simmons, Leonard H van den Berg. Nat Rev Dis Primers 2017
18
Neurodegeneration. C9ORF72 repeat expansions in mice cause TDP-43 pathology, neuronal loss, and behavioral deficits.
Jeannie Chew, Tania F Gendron, Mercedes Prudencio, Hiroki Sasaguri, Yong-Jie Zhang, Monica Castanedes-Casey, Chris W Lee, Karen Jansen-West, Aishe Kurti, Melissa E Murray,[...]. Science 2015
Jeannie Chew, Tania F Gendron, Mercedes Prudencio, Hiroki Sasaguri, Yong-Jie Zhang, Monica Castanedes-Casey, Chris W Lee, Karen Jansen-West, Aishe Kurti, Melissa E Murray,[...]. Science 2015
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Susceptibility of Mutant SOD1 to Form a Destabilized Monomer Predicts Cellular Aggregation and Toxicity but Not In vitro Aggregation Propensity.
Luke McAlary, J Andrew Aquilina, Justin J Yerbury. Front Neurosci 2016
Luke McAlary, J Andrew Aquilina, Justin J Yerbury. Front Neurosci 2016
18
Supersaturation is a major driving force for protein aggregation in neurodegenerative diseases.
Prajwal Ciryam, Rishika Kundra, Richard I Morimoto, Christopher M Dobson, Michele Vendruscolo. Trends Pharmacol Sci 2015
Prajwal Ciryam, Rishika Kundra, Richard I Morimoto, Christopher M Dobson, Michele Vendruscolo. Trends Pharmacol Sci 2015
18
Exome sequencing reveals VCP mutations as a cause of familial ALS.
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18
TDP-43 is a component of ubiquitin-positive tau-negative inclusions in frontotemporal lobar degeneration and amyotrophic lateral sclerosis.
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18
Overexpression of human wild-type FUS causes progressive motor neuron degeneration in an age- and dose-dependent fashion.
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18
Therapeutic reduction of ataxin-2 extends lifespan and reduces pathology in TDP-43 mice.
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18
Mutations in UBQLN2 cause dominant X-linked juvenile and adult-onset ALS and ALS/dementia.
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18
Autophagy Dysregulation in ALS: When Protein Aggregates Get Out of Hand.
Nandini Ramesh, Udai Bhan Pandey. Front Mol Neurosci 2017
Nandini Ramesh, Udai Bhan Pandey. Front Mol Neurosci 2017
18
Neuroblastoma x spinal cord (NSC) hybrid cell lines resemble developing motor neurons.
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18
Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation.
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18
Mutations in FUS, an RNA processing protein, cause familial amyotrophic lateral sclerosis type 6.
Caroline Vance, Boris Rogelj, Tibor Hortobágyi, Kurt J De Vos, Agnes Lumi Nishimura, Jemeen Sreedharan, Xun Hu, Bradley Smith, Deborah Ruddy, Paul Wright,[...]. Science 2009
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18
Prion-Like Propagation of Protein Misfolding and Aggregation in Amyotrophic Lateral Sclerosis.
Luke McAlary, Steven S Plotkin, Justin J Yerbury, Neil R Cashman. Front Mol Neurosci 2019
Luke McAlary, Steven S Plotkin, Justin J Yerbury, Neil R Cashman. Front Mol Neurosci 2019
18
Animal models of amyotrophic lateral sclerosis: A comparison of model validity.
Jessica R Morrice, Cheryl Y Gregory-Evans, Christopher A Shaw. Neural Regen Res 2018
Jessica R Morrice, Cheryl Y Gregory-Evans, Christopher A Shaw. Neural Regen Res 2018
18
Antisense oligonucleotides extend survival and reverse decrement in muscle response in ALS models.
Alex McCampbell, Tracy Cole, Amy J Wegener, Giulio S Tomassy, Amy Setnicka, Brandon J Farley, Kathleen M Schoch, Mariah L Hoye, Mark Shabsovich, Linhong Sun,[...]. J Clin Invest 2018
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18
The C9orf72 repeat expansion disrupts nucleocytoplasmic transport.
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18
Key role of UBQLN2 in pathogenesis of amyotrophic lateral sclerosis and frontotemporal dementia.
Laurence Renaud, Vincent Picher-Martel, Philippe Codron, Jean-Pierre Julien. Acta Neuropathol Commun 2019
Laurence Renaud, Vincent Picher-Martel, Philippe Codron, Jean-Pierre Julien. Acta Neuropathol Commun 2019
13
The proteostasis network and its decline in ageing.
Mark S Hipp, Prasad Kasturi, F Ulrich Hartl. Nat Rev Mol Cell Biol 2019
Mark S Hipp, Prasad Kasturi, F Ulrich Hartl. Nat Rev Mol Cell Biol 2019
13
Pathways of cellular proteostasis in aging and disease.
Courtney L Klaips, Gopal Gunanathan Jayaraj, F Ulrich Hartl. J Cell Biol 2018
Courtney L Klaips, Gopal Gunanathan Jayaraj, F Ulrich Hartl. J Cell Biol 2018
13
A Drosophila model of FUS-related neurodegeneration reveals genetic interaction between FUS and TDP-43.
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13
Analysis of amyotrophic lateral sclerosis as a multistep process: a population-based modelling study.
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13
Amyotrophic lateral sclerosis.
Orla Hardiman, Ammar Al-Chalabi, Adriano Chio, Emma M Corr, Giancarlo Logroscino, Wim Robberecht, Pamela J Shaw, Zachary Simmons, Leonard H van den Berg. Nat Rev Dis Primers 2017
Orla Hardiman, Ammar Al-Chalabi, Adriano Chio, Emma M Corr, Giancarlo Logroscino, Wim Robberecht, Pamela J Shaw, Zachary Simmons, Leonard H van den Berg. Nat Rev Dis Primers 2017
13
Stages of pTDP-43 pathology in amyotrophic lateral sclerosis.
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13
Proteomics Approaches for Biomarker and Drug Target Discovery in ALS and FTD.
Thomas J Hedl, Rebecca San Gil, Flora Cheng, Stephanie L Rayner, Jennilee M Davidson, Alana De Luca, Maria D Villalva, Heath Ecroyd, Adam K Walker, Albert Lee. Front Neurosci 2019
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13
Distinct partitioning of ALS associated TDP-43, FUS and SOD1 mutants into cellular inclusions.
Natalie E Farrawell, Isabella A Lambert-Smith, Sadaf T Warraich, Ian P Blair, Darren N Saunders, Danny M Hatters, Justin J Yerbury. Sci Rep 2015
Natalie E Farrawell, Isabella A Lambert-Smith, Sadaf T Warraich, Ian P Blair, Darren N Saunders, Danny M Hatters, Justin J Yerbury. Sci Rep 2015
13
The genotype-phenotype landscape of familial amyotrophic lateral sclerosis in Australia.
E P McCann, K L Williams, J A Fifita, I S Tarr, J O'Connor, D B Rowe, G A Nicholson, I P Blair. Clin Genet 2017
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13
Genome-wide Analyses Identify KIF5A as a Novel ALS Gene.
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13
Massive transcriptome sequencing of human spinal cord tissues provides new insights into motor neuron degeneration in ALS.
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13
Mutations of optineurin in amyotrophic lateral sclerosis.
Hirofumi Maruyama, Hiroyuki Morino, Hidefumi Ito, Yuishin Izumi, Hidemasa Kato, Yasuhito Watanabe, Yoshimi Kinoshita, Masaki Kamada, Hiroyuki Nodera, Hidenori Suzuki,[...]. Nature 2010
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13
Neuronal Expression of UBQLN2P497H Exacerbates TDP-43 Pathology in TDP-43G348C Mice through Interaction with Ubiquitin.
Vincent Picher-Martel, Laurence Renaud, Christine Bareil, Jean-Pierre Julien. Mol Neurobiol 2019
Vincent Picher-Martel, Laurence Renaud, Christine Bareil, Jean-Pierre Julien. Mol Neurobiol 2019
25
CCNF mutations in amyotrophic lateral sclerosis and frontotemporal dementia.
Kelly L Williams, Simon Topp, Shu Yang, Bradley Smith, Jennifer A Fifita, Sadaf T Warraich, Katharine Y Zhang, Natalie Farrawell, Caroline Vance, Xun Hu,[...]. Nat Commun 2016
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13
Widespread aggregation and neurodegenerative diseases are associated with supersaturated proteins.
Prajwal Ciryam, Gian Gaetano Tartaglia, Richard I Morimoto, Christopher M Dobson, Michele Vendruscolo. Cell Rep 2013
Prajwal Ciryam, Gian Gaetano Tartaglia, Richard I Morimoto, Christopher M Dobson, Michele Vendruscolo. Cell Rep 2013
13
The metastability of the proteome of spinal motor neurons underlies their selective vulnerability in ALS.
Justin J Yerbury, Lezanne Ooi, Ian P Blair, Prajwal Ciryam, Christopher M Dobson, Michele Vendruscolo. Neurosci Lett 2019
Justin J Yerbury, Lezanne Ooi, Ian P Blair, Prajwal Ciryam, Christopher M Dobson, Michele Vendruscolo. Neurosci Lett 2019
18
ALS Genes in the Genomic Era and their Implications for FTD.
Hung Phuoc Nguyen, Christine Van Broeckhoven, Julie van der Zee. Trends Genet 2018
Hung Phuoc Nguyen, Christine Van Broeckhoven, Julie van der Zee. Trends Genet 2018
13
Prion-like properties of pathological TDP-43 aggregates from diseased brains.
Takashi Nonaka, Masami Masuda-Suzukake, Tetsuaki Arai, Yoko Hasegawa, Hiroyasu Akatsu, Tomokazu Obi, Mari Yoshida, Shigeo Murayama, David M A Mann, Haruhiko Akiyama,[...]. Cell Rep 2013
Takashi Nonaka, Masami Masuda-Suzukake, Tetsuaki Arai, Yoko Hasegawa, Hiroyasu Akatsu, Tomokazu Obi, Mari Yoshida, Shigeo Murayama, David M A Mann, Haruhiko Akiyama,[...]. Cell Rep 2013
13
SQSTM1 mutations in familial and sporadic amyotrophic lateral sclerosis.
Faisal Fecto, Jianhua Yan, S Pavan Vemula, Erdong Liu, Yi Yang, Wenjie Chen, Jian Guo Zheng, Yong Shi, Nailah Siddique, Hasan Arrat,[...]. Arch Neurol 2011
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13
Walking the tightrope: proteostasis and neurodegenerative disease.
Justin J Yerbury, Lezanne Ooi, Andrew Dillin, Darren N Saunders, Danny M Hatters, Philip M Beart, Neil R Cashman, Mark R Wilson, Heath Ecroyd. J Neurochem 2016
Justin J Yerbury, Lezanne Ooi, Andrew Dillin, Darren N Saunders, Danny M Hatters, Philip M Beart, Neil R Cashman, Mark R Wilson, Heath Ecroyd. J Neurochem 2016
13
Co-cited is the co-citation frequency, indicating how many articles cite the article together with the query article. Similarity is the co-citation as percentage of the times cited of the query article or the article in the search results, whichever is the lowest. These numbers are calculated for the last 100 citations when articles are cited more than 100 times.