Jie Xu, Alessandra Livraghi-Butrico, Xia Hou, Carthic Rajagopalan, Jifeng Zhang, Jun Song, Hong Jiang, Hong-Guang Wei, Hui Wang, Mohamad Bouhamdan, Jinxue Ruan, Dongshan Yang, Yining Qiu, Youming Xie, Ronald Barrett, Sharon McClellan, Hongmei Mou, Qingtian Wu, Xuequn Chen, Troy D Rogers, Kristen J Wilkinson, Rodney C Gilmore, Charles R Esther, Khalequz Zaman, Xiubin Liang, Michael Sobolic, Linda Hazlett, Kezhong Zhang, Raymond A Frizzell, Martina Gentzsch, Wanda K O'Neal, Barbara R Grubb, Y Eugene Chen, Richard C Boucher, Fei Sun. JCI Insight 2021
Times Cited: 12
Times Cited: 12
Times Cited
Times Co-cited
Similarity
Disease phenotype of a ferret CFTR-knockout model of cystic fibrosis.
Xingshen Sun, Hongshu Sui, John T Fisher, Ziying Yan, Xiaoming Liu, Hyung-Ju Cho, Nam Soo Joo, Yulong Zhang, Weihong Zhou, Yaling Yi,[...]. J Clin Invest 2010
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A sheep model of cystic fibrosis generated by CRISPR/Cas9 disruption of the CFTR gene.
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Origins of cystic fibrosis lung disease.
David A Stoltz, David K Meyerholz, Michael J Welsh. N Engl J Med 2015
David A Stoltz, David K Meyerholz, Michael J Welsh. N Engl J Med 2015
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Elexacaftor-Tezacaftor-Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele.
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CRISPR-Based Adenine Editors Correct Nonsense Mutations in a Cystic Fibrosis Organoid Biobank.
Maarten H Geurts, Eyleen de Poel, Gimano D Amatngalim, Rurika Oka, Fleur M Meijers, Evelien Kruisselbrink, Peter van Mourik, Gitte Berkers, Karin M de Winter-de Groot, Sabine Michel,[...]. Cell Stem Cell 2020
Maarten H Geurts, Eyleen de Poel, Gimano D Amatngalim, Rurika Oka, Fleur M Meijers, Evelien Kruisselbrink, Peter van Mourik, Gitte Berkers, Karin M de Winter-de Groot, Sabine Michel,[...]. Cell Stem Cell 2020
33
Characterization of two rat models of cystic fibrosis-KO and F508del CFTR-Generated by Crispr-Cas9.
Elise Dreano, Marc Bacchetta, Juliette Simonin, Louise Galmiche, Claire Usal, Lotfi Slimani, Jérémy Sadoine, Laurent Tesson, Ignacio Anegon, Jean-Paul Concordet,[...]. Animal Model Exp Med 2019
Elise Dreano, Marc Bacchetta, Juliette Simonin, Louise Galmiche, Claire Usal, Lotfi Slimani, Jérémy Sadoine, Laurent Tesson, Ignacio Anegon, Jean-Paul Concordet,[...]. Animal Model Exp Med 2019
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Efficient Gene Editing at Major CFTR Mutation Loci.
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Jinxue Ruan, Hiroyuki Hirai, Dongshan Yang, Linyuan Ma, Xia Hou, Hong Jiang, Hongguang Wei, Carthic Rajagopalan, Hongmei Mou, Guoshun Wang,[...]. Mol Ther Nucleic Acids 2019
25
Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial.
Harry G M Heijerman, Edward F McKone, Damian G Downey, Eva Van Braeckel, Steven M Rowe, Elizabeth Tullis, Marcus A Mall, John J Welter, Bonnie W Ramsey, Charlotte M McKee,[...]. Lancet 2019
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Pathophysiology of gene-targeted mouse models for cystic fibrosis.
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Phenotypic Characterization and Comparison of Cystic Fibrosis Rat Models Generated Using CRISPR/Cas9 Gene Editing.
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Alexandra McCarron, Patricia Cmielewski, Nicole Reyne, Chantelle McIntyre, John Finnie, Fiona Craig, Nathan Rout-Pitt, Juliette Delhove, John E Schjenken, Hon Y Chan,[...]. Am J Pathol 2020
25
In utero and postnatal VX-770 administration rescues multiorgan disease in a ferret model of cystic fibrosis.
Xingshen Sun, Yaling Yi, Ziying Yan, Bradley H Rosen, Bo Liang, Michael C Winter, T Idil Apak Evans, Pavana G Rotti, Yu Yang, Jaimie S Gray,[...]. Sci Transl Med 2019
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Disruption of the CFTR gene produces a model of cystic fibrosis in newborn pigs.
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25
CFTR dysregulation drives active selection of the gut microbiome.
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25
A BAC Transgene Expressing Human CFTR under Control of Its Regulatory Elements Rescues Cftr Knockout Mice.
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Functional repair of CFTR by CRISPR/Cas9 in intestinal stem cell organoids of cystic fibrosis patients.
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25
Impaired mucus detachment disrupts mucociliary transport in a piglet model of cystic fibrosis.
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Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth.
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Animal and model systems for studying cystic fibrosis.
Bradley H Rosen, Marc Chanson, Lara R Gawenis, Jinghua Liu, Aderonke Sofoluwe, Alice Zoso, John F Engelhardt. J Cyst Fibros 2018
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Production of immunodeficient rabbits by multiplex embryo transfer and multiplex gene targeting.
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16
RS-1 enhances CRISPR/Cas9- and TALEN-mediated knock-in efficiency.
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Effective gene targeting in rabbits using RNA-guided Cas9 nucleases.
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High-Efficiency, Selection-free Gene Repair in Airway Stem Cells from Cystic Fibrosis Patients Rescues CFTR Function in Differentiated Epithelia.
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A mouse model for the cystic fibrosis delta F508 mutation.
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Human apolipoprotein A-II protects against diet-induced atherosclerosis in transgenic rabbits.
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Understanding how cystic fibrosis mutations disrupt CFTR function: from single molecules to animal models.
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Expression of human apoAII in transgenic rabbits leads to dyslipidemia: a new model for combined hyperlipidemia.
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16
New animal models of cystic fibrosis: what are they teaching us?
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Generation and characterization of a delta F508 cystic fibrosis mouse model.
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A mouse model for the delta F508 allele of cystic fibrosis.
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Increased high-density lipoprotein levels caused by a common cholesteryl-ester transfer protein gene mutation.
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A novel rabbit model of Duchenne muscular dystrophy generated by CRISPR/Cas9.
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Rabbit models for the study of human atherosclerosis: from pathophysiological mechanisms to translational medicine.
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An animal model for cystic fibrosis made by gene targeting.
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Cystic fibrosis mice carrying the missense mutation G551D replicate human genotype-phenotype correlations.
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Co-cited is the co-citation frequency, indicating how many articles cite the article together with the query article. Similarity is the co-citation as percentage of the times cited of the query article or the article in the search results, whichever is the lowest. These numbers are calculated for the last 100 citations when articles are cited more than 100 times.