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List of shared articles
Times cited
The Clinical Concept of LTDpathy: Is Dysregulated LTD Responsible for Prodromal Cerebellar Symptoms?
Hiroshi Mitoma, Kazuhiko Yamaguchi, Jerome Honnorat, Mario Manto. Brain Sci 2022
Hiroshi Mitoma, Kazuhiko Yamaguchi, Jerome Honnorat, Mario Manto. Brain Sci 2022
Combined overexpression of ATXN1L and mutant ATXN1 knockdown by AAV rescue motor phenotypes and gene signatures in SCA1 mice.
Ellie M Carrell, Megan S Keiser, Ashley B Robbins, Beverly L Davidson. Mol Ther Methods Clin Dev 2022
Ellie M Carrell, Megan S Keiser, Ashley B Robbins, Beverly L Davidson. Mol Ther Methods Clin Dev 2022
Region-specific preservation of Purkinje cell morphology and motor behavior in the ATXN1[82Q] mouse model of spinocerebellar ataxia 1.
Joshua J White, Laurens W J Bosman, Francois G C Blot, Catarina Osório, Bram W Kuppens, Wilhelmina H J J Krijnen, Charlotte Andriessen, Chris I De Zeeuw, Dick Jaarsma, Martijn Schonewille. Brain Pathol 2021
Joshua J White, Laurens W J Bosman, Francois G C Blot, Catarina Osório, Bram W Kuppens, Wilhelmina H J J Krijnen, Charlotte Andriessen, Chris I De Zeeuw, Dick Jaarsma, Martijn Schonewille. Brain Pathol 2021
Gene Deregulation and Underlying Mechanisms in Spinocerebellar Ataxias With Polyglutamine Expansion.
Anna Niewiadomska-Cimicka, Antoine Hache, Yvon Trottier. Front Neurosci 2020
Anna Niewiadomska-Cimicka, Antoine Hache, Yvon Trottier. Front Neurosci 2020
Disrupted Calcium Signaling in Animal Models of Human Spinocerebellar Ataxia (SCA).
Francesca Prestori, Francesco Moccia, Egidio D'Angelo. Int J Mol Sci 2019
Francesca Prestori, Francesco Moccia, Egidio D'Angelo. Int J Mol Sci 2019
Spinocerebellar Ataxia Type 1: Molecular Mechanisms of Neurodegeneration and Preclinical Studies.
Judit M Pérez Ortiz, Harry T Orr. Adv Exp Med Biol 2018
Judit M Pérez Ortiz, Harry T Orr. Adv Exp Med Biol 2018
Spinocerebellar [corrected] Ataxia Type 6: Molecular Mechanisms and Calcium Channel Genetics.
Xiaofei Du, Christopher Manuel Gomez. Adv Exp Med Biol 2018
Xiaofei Du, Christopher Manuel Gomez. Adv Exp Med Biol 2018
Progressive impairment of cerebellar mGluR signalling and its therapeutic potential for cerebellar ataxia in spinocerebellar ataxia type 1 model mice.
Anton N Shuvaev, Nobutake Hosoi, Yamato Sato, Dai Yanagihara, Hirokazu Hirai. J Physiol 2017
Anton N Shuvaev, Nobutake Hosoi, Yamato Sato, Dai Yanagihara, Hirokazu Hirai. J Physiol 2017
Type-1 metabotropic glutamate receptor signaling in cerebellar Purkinje cells in health and disease.
Masanobu Kano, Takaki Watanabe. F1000Res 2017
Masanobu Kano, Takaki Watanabe. F1000Res 2017
Motor and Cerebellar Architectural Abnormalities during the Early Progression of Ataxia in a Mouse Model of SCA1 and How Early Prevention Leads to a Better Outcome Later in Life.
Mohamed F Ibrahim, Emmet M Power, Kay Potapov, Ruth M Empson. Front Cell Neurosci 2017
Mohamed F Ibrahim, Emmet M Power, Kay Potapov, Ruth M Empson. Front Cell Neurosci 2017
Developmental YAPdeltaC determines adult pathology in a model of spinocerebellar ataxia type 1.
Kyota Fujita, Ying Mao, Shigenori Uchida, Xigui Chen, Hiroki Shiwaku, Takuya Tamura, Hikaru Ito, Kei Watase, Hidenori Homma, Kazuhiko Tagawa,[...]. Nat Commun 2017
Kyota Fujita, Ying Mao, Shigenori Uchida, Xigui Chen, Hiroki Shiwaku, Takuya Tamura, Hikaru Ito, Kei Watase, Hidenori Homma, Kazuhiko Tagawa,[...]. Nat Commun 2017
Impaired mTORC1-Dependent Expression of Homer-3 Influences SCA1 Pathophysiology.
Céline Ruegsegger, David M Stucki, Silvio Steiner, Nico Angliker, Julika Radecke, Eva Keller, Benoît Zuber, Markus A Rüegg, Smita Saxena. Neuron 2016
Céline Ruegsegger, David M Stucki, Silvio Steiner, Nico Angliker, Julika Radecke, Eva Keller, Benoît Zuber, Markus A Rüegg, Smita Saxena. Neuron 2016
Cellular and circuit mechanisms underlying spinocerebellar ataxias.
Pratap Meera, Stefan M Pulst, Thomas S Otis. J Physiol 2016
Pratap Meera, Stefan M Pulst, Thomas S Otis. J Physiol 2016
Abnormalities in synaptic dynamics during development in a mouse model of spinocerebellar ataxia type 1.
Yusuke Hatanaka, Kei Watase, Keiji Wada, Yoshitaka Nagai. Sci Rep 2015
Yusuke Hatanaka, Kei Watase, Keiji Wada, Yoshitaka Nagai. Sci Rep 2015
Pharmacological enhancement of mGlu1 metabotropic glutamate receptors causes a prolonged symptomatic benefit in a mouse model of spinocerebellar ataxia type 1.
Serena Notartomaso, Cristina Zappulla, Francesca Biagioni, Milena Cannella, Domenico Bucci, Giada Mascio, Pamela Scarselli, Francesco Fazio, Filippo Weisz, Luana Lionetto,[...]. Mol Brain 2013
Serena Notartomaso, Cristina Zappulla, Francesca Biagioni, Milena Cannella, Domenico Bucci, Giada Mascio, Pamela Scarselli, Francesco Fazio, Filippo Weisz, Luana Lionetto,[...]. Mol Brain 2013