A citation-based method for searching scientific literature

Causative role of oxidative stress in a Drosophila model of Friedreich ataxia.
José V Llorens, Juan A Navarro, Maria J Martínez-Sebastián, Mary K Baylies, S Schneuwly, José A Botella, Maria D Moltó. FASEB J 2007
Times Cited: 93



Frataxin is reduced in Friedreich ataxia patients and is associated with mitochondrial membranes.
V Campuzano, L Montermini, Y Lutz, L Cova, C Hindelang, S Jiralerspong, Y Trottier, S J Kish, B Faucheux, P Trouillas, F J Authier, A Dürr, J L Mandel, A Vescovi, M Pandolfo, M Koenig. Hum Mol Genet 1997
Times Cited: 555




List of shared articles



Times cited

Overexpression of human and fly frataxins in Drosophila provokes deleterious effects at biochemical, physiological and developmental levels.
Juan A Navarro, José V Llorens, Sirena Soriano, José A Botella, Stephan Schneuwly, María J Martínez-Sebastián, María D Moltó. PLoS One 2011
28

Altered lipid metabolism in a Drosophila model of Friedreich's ataxia.
Juan A Navarro, Elisabeth Ohmann, Diego Sanchez, José A Botella, Gerhard Liebisch, María D Moltó, María D Ganfornina, Gerd Schmitz, Stephan Schneuwly. Hum Mol Genet 2010
70

Pathophysiogical and therapeutic progress in Friedreich ataxia.
H Puccio, M Anheim, C Tranchant. Rev Neurol (Paris) 2014
19

The NRF2 Signaling Network Defines Clinical Biomarkers and Therapeutic Opportunity in Friedreich's Ataxia.
Piergiorgio La Rosa, Enrico Silvio Bertini, Fiorella Piemonte. Int J Mol Sci 2020
15

Using human pluripotent stem cells to study Friedreich ataxia cardiomyopathy.
Duncan E Crombie, Martin F Pera, Martin B Delatycki, Alice Pébay. Int J Cardiol 2016
4

The Role of Iron in Friedreich's Ataxia: Insights From Studies in Human Tissues and Cellular and Animal Models.
José Vicente Llorens, Sirena Soriano, Pablo Calap-Quintana, Pilar Gonzalez-Cabo, María Dolores Moltó. Front Neurosci 2019
35

Time-resolved functional analysis of acute impairment of frataxin expression in an inducible cell model of Friedreich ataxia.
Dörte Poburski, Josefine Barbara Boerner, Michel Koenig, Michael Ristow, René Thierbach. Biol Open 2016
15

Understanding the genetic and molecular pathogenesis of Friedreich's ataxia through animal and cellular models.
Alain Martelli, Marek Napierala, Hélène Puccio. Dis Model Mech 2012
49

Understanding the molecular mechanisms of Friedreich's ataxia to develop therapeutic approaches.
Stéphane Schmucker, Hélène Puccio. Hum Mol Genet 2010
92

Friedreich ataxia: molecular mechanisms, redox considerations, and therapeutic opportunities.
Renata Santos, Sophie Lefevre, Dominika Sliwa, Alexandra Seguin, Jean-Michel Camadro, Emmanuel Lesuisse. Antioxid Redox Signal 2010
123

Chronochemistry in neurodegeneration.
Annalisa Pastore, Salvatore Adinolfi. Front Mol Neurosci 2014
7

Mitochondrial dysfunction induced by frataxin deficiency is associated with cellular senescence and abnormal calcium metabolism.
Arantxa Bolinches-Amorós, Belén Mollá, David Pla-Martín, Francesc Palau, Pilar González-Cabo. Front Cell Neurosci 2014
52

Mitoferrin modulates iron toxicity in a Drosophila model of Friedreich's ataxia.
Juan A Navarro, Jose A Botella, Christoph Metzendorf, Maria I Lind, Stephan Schneuwly. Free Radic Biol Med 2015
38

Oxidative stress in inherited mitochondrial diseases.
Genki Hayashi, Gino Cortopassi. Free Radic Biol Med 2015
93

Friedreich ataxia: new pathways.
Massimo Pandolfo. J Child Neurol 2012
20

Drosophila melanogaster Models of Friedreich's Ataxia.
P Calap-Quintana, J A Navarro, J González-Fernández, M J Martínez-Sebastián, M D Moltó, J V Llorens. Biomed Res Int 2018
7

Friedreich ataxia: an update on animal models, frataxin function and therapies.
Pilar González-Cabo, José Vicente Llorens, Francesc Palau, Maria Dolores Moltó. Adv Exp Med Biol 2009
12

Lentivirus-meditated frataxin gene delivery reverses genome instability in Friedreich ataxia patient and mouse model fibroblasts.
H Khonsari, M Schneider, S Al-Mahdawi, Y G Chianea, M Themis, C Parris, M A Pook, M Themis. Gene Ther 2016
7

Defining Transcription Regulatory Elements in the Human Frataxin Gene: Implications for Gene Therapy.
Jixue Li, Yanjie Li, Jun Wang, Trevor J Gonzalez, Aravind Asokan, Jill S Napierala, Marek Napierala. Hum Gene Ther 2020
5

Dysregulation of cellular iron metabolism in Friedreich ataxia: from primary iron-sulfur cluster deficit to mitochondrial iron accumulation.
Alain Martelli, Hélène Puccio. Front Pharmacol 2014
90

Iron in Friedreich Ataxia: A Central Role in the Pathophysiology or an Epiphenomenon?
David Alsina, Rosa Purroy, Joaquim Ros, Jordi Tamarit. Pharmaceuticals (Basel) 2018
19

Hydrogen peroxide scavenging rescues frataxin deficiency in a Drosophila model of Friedreich's ataxia.
Peter R Anderson, Kim Kirby, William C Orr, Arthur J Hilliker, John P Phillips. Proc Natl Acad Sci U S A 2008
84

Reversible Axonal Dystrophy by Calcium Modulation in Frataxin-Deficient Sensory Neurons of YG8R Mice.
Belén Mollá, Diana C Muñoz-Lasso, Fátima Riveiro, Arantxa Bolinches-Amorós, Federico V Pallardó, Angel Fernandez-Vilata, María de la Iglesia-Vaya, Francesc Palau, Pilar Gonzalez-Cabo. Front Mol Neurosci 2017
23

Impaired nuclear Nrf2 translocation undermines the oxidative stress response in Friedreich ataxia.
Vincent Paupe, Emmanuel P Dassa, Sergio Goncalves, Françoise Auchère, Maria Lönn, Arne Holmgren, Pierre Rustin. PLoS One 2009
145

Oxidative stress and altered lipid metabolism in Friedreich ataxia.
Jordi Tamarit, Èlia Obis, Joaquim Ros. Free Radic Biol Med 2016
37

Antioxidant Therapies and Oxidative Stress in Friedreich´s Ataxia: The Right Path or Just a Diversion?
Laura R Rodríguez, Tamara Lapeña, Pablo Calap-Quintana, María Dolores Moltó, Pilar Gonzalez-Cabo, Juan Antonio Navarro Langa. Antioxidants (Basel) 2020
7

The first cellular models based on frataxin missense mutations that reproduce spontaneously the defects associated with Friedreich ataxia.
Nadège Calmels, Stéphane Schmucker, Marie Wattenhofer-Donzé, Alain Martelli, Nadège Vaucamps, Laurence Reutenauer, Nadia Messaddeq, Cécile Bouton, Michel Koenig, Hélène Puccio. PLoS One 2009
42

Mitofusin-Dependent ER Stress Triggers Glial Dysfunction and Nervous System Degeneration in a Drosophila Model of Friedreich's Ataxia.
Oliver Edenharter, Stephan Schneuwly, Juan A Navarro. Front Mol Neurosci 2018
22


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